Show Menu

Cystic Fibrosis (Obstructive) Cheat Sheet (DRAFT) by

ACNP CheatSheet

This is a draft cheat sheet. It is a work in progress and is not finished yet.

Cystic Fibrosis

Auto­somal recess­ive predom­inantly in white patients. Defect in chloride channel protein causes impaired chloride and water transport, which leads to exce­ssively thick, vicious secret­ions in the respir­atory tract, exocrine pancreas, sweat glands, GI, and GU tracts.
• Prognosis has improved with the median age of death now >30.
• Pancreatic enzyme replac­ement, fat-so­luble vitamin supple­ments, chest PT, vaccin­ations (influenza and pneumo­coc­cal), antibi­otics for infect­ions, inhaled recomb­inant human deoxyr­ibo­nuc­lease (rhDNAse) breaks does the DNA in respir­atory mucus that clogs airways.
• Results in obst­ructive lung disease with chronic infect­ions (frequ­ently Pseudo­monas), pancreatic insuff­ici­ency, and other GI compli­cat­ions.



Help Us Go Positive!

We offset our carbon usage with Ecologi. Click the link below to help us!

We offset our carbon footprint via Ecologi